Definition Background Congenital Long QT Syndrome (LQTS) may occur with (Jervell and Lange-Nielsen syndrome) or without (Romano-Ward syndrome) deafness. Presents as lightheadedness, syncope, torsades, and cardiac arrest. May be triggered by adrenergic stimulation or even auditory stimulation (LQT1 and 2). Three ion channel abnormalities have been identified – LQT1 and LQT2 (K+), and LQT3 (Na+). […]